Congenital Syngnathia; Turmoils and Tragedy
نویسندگان
چکیده
Congenital syngnathia is an extremely rare condition with no standardized treatment. We hereby report a case highlighting the difficulties faced in its management and the postoperative complications.
منابع مشابه
An Unusual Case of Congenital Syngnathia
Congenital syngnathia is a rare anomaly characterised by the presence of soft tissue (synechia) or bony adhesions (synostosis) between the maxilla and mandible. A wide spectrum and range of severity have been documented in case reports. Primarily it manifests in the inability to open the mouth; impacting on mandibular growth, nutrition, speech and management of the airway. The bony adhesions ca...
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Syngnathia (bony fusion of the upper and lower jaw) is a rare human congenital condition, with fewer than sixty cases reported in the literature. Syngnathia typically presents as part of a complex syndrome comprising widespread oral and maxillofacial anomalies, but it can also occur in isolation. Most cartilage, bone, and connective tissue of the head and face is derived from neural crest cells...
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Congenital fusion of the maxilla and the mandible is a rare condition. The extent of the problem ranges from simple mucosal adhesion (synechia) to severe bony fusion (syngnathia). Here we present a patient with zygomatico-mandibular fusion who was treated at neonatal and infancy periods at three different stages without tracheostomy. Having had recurrence for two times, porcine grafting was per...
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A 5-day-old newborn, product of non-consanguineous marriage, presented with inability to completely open oral cavity and feeding difficulty. On examination, there was a good sucking reflex and limited mouth opening (Fig. A) with retrognathia (Fig. B). Maxillary CT with 3D reconstruction revealed hypoplasia of the ascending branches of the mandible; the temporomandibular joints were normal (Fig....
متن کاملIsolated congenital maxillomandibular synechiae.
INTRODUCTION Congenital maxillomandibular syngnathia, or fusion of the jaws, is a rare condition that has a broad spectrum of presentations. The restricted mouth opening can lead to issues with feeding, swallowing, and respiration resulting in failure to thrive and temporomandibular joint ankylosis. Early recognition and treatment is necessary for proper growth and development. CASE REPORT We...
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عنوان ژورنال:
دوره 6 شماره
صفحات -
تاریخ انتشار 2017